Liver transplantation for cardiac failure in patients with hereditary hemorrhagic telangiectasia.

نویسندگان

  • Thierry Thevenot
  • Claire Vanlemmens
  • Vincent Di Martino
  • Marie-Claude Becker
  • Pierre-Olivier Denue
  • Bernadette Kantelip
  • Solange Bresson-Hadni
  • Bruno Heyd
  • Georges Mantion
  • Jean-Philippe Miguet
چکیده

Liver involvement in hereditary hemorrhagic telangiectasia may lead to high-output cardiac failure. Few data have been reported on orthotopic liver transplantation (OLT) for these patients. In this paper, we describe two patients treated by OLT as a salvage procedure for cardiac failure, and we review literature on this subject. Our two patients resumed normal cardiac function after OLT. This procedure appears to be a promising therapy with good long-term results despite dissection difficulties encountered due to the collateral arterial network reorganization.

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عنوان ژورنال:
  • Liver transplantation : official publication of the American Association for the Study of Liver Diseases and the International Liver Transplantation Society

دوره 11 7  شماره 

صفحات  -

تاریخ انتشار 2005